Host: Rabbit
Target Protein: Bone Alkaline Phosphatase
IR: Immunogen Range:56-150/524
Clonality: Polyclonal
Isotype: IgG
Entrez Gene: 249
Swiss Prot: P05186
Source: KLH conjugated synthetic peptide derived from human Bone Alkaline Phosphatase:56-150/524
Purification: affinity purified by Protein A
Storage: 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
Background: Defects in ALPL are a cause of hypophosphatasia (HOPS) . HOPS is an inherited metabolic bone disease characterized by defective skeletal mineralization. Four hypophosphatasia forms are distinguished, depending on the age of onset: perinatal, infantile, childhood and adult type. The perinatal form is the most severe and is almost always fatal. Patients with only premature loss of deciduous teeth, but with no bone disease are regarded as having odontohypophosphatasia.
Size: 200ul
Concentration: 1mg/ml
Applications: WB=1:500-2000, IHC-P=1:100-500, IHC-F=1:100-500, IF=1:100-500, Flow-Cyt=1ug/Test, ELISA=1:5000-10000
Cross Reactive Species: Mouse,Human (predicted: Rabbit,Cow,Rat)
For research use only. Not intended for diagnostic or therapeutic use.