bs-14034R [Primary Antibody]
Rabbit  Anti-CPS1  Polyclonal Antibody
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Host: Rabbit

Target Protein: CPS1

IR: Immunogen Range:1351-1500/1500

Clonality: Polyclonal

Isotype: IgG

Entrez Gene: 1373

Swiss Prot: P31327

Source: KLH conjugated synthetic peptide derived from human CPS1:1351-1500/1500 

Purification: affinity purified by Protein A

Storage: 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.

Background: The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]

Size: 200ul

Concentration: 1mg/ml

Applications: IHC-P=1:100-500, IHC-F=1:100-500, ICC=1:100-500, IF=1:100-500, ELISA=1:5000-10000

Cross Reactive Species: Rat (predicted: Human,Mouse,Dog,Sheep)

For research use only. Not intended for diagnostic or therapeutic use.

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