| 产品编号 |
bs-42132P |
| 英文名称 |
Recombinant mouse ACOX1 protein, C-His
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| 中文名称 |
重组小鼠过氧化物酶酰基辅酶A氧化酶1蛋白 |
| 别 名 |
ACOX1; ACOX1_HUMAN; ACOX1_MOUSE; AOX antibody Palmitoyl CoA oxidase; Palmitoyl-CoA oxidase; Peroxisomal acyl coenzyme A oxidase 1; Peroxisomal acyl-coenzyme A oxidase 1; SCOX; Straight chain acyl CoA oxidase; Straight-chain acyl-CoA oxidase.
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| 克 隆 号 |
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| 理论分子量 |
31.8 kDa |
| 检测分子量 |
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| 性 状 |
Lyophilized or Liquid |
| 浓 度 |
>0.5mg/ml |
| 物 种 |
Mouse |
| 序 列 |
386-661/661 |
| 纯 度 |
>90% as determined by SDS-PAGE |
| 表达系统 |
E.coli |
| 活性 |
Not tested |
| 标签 |
C-His |
| 缓 冲 液 |
20mM Tris-HCl (pH8.0)with 8M Urea. |
| 保存条件 |
Stored at -70℃ or -20℃. Avoid repeated freeze/thaw cycles. |
| 注意事项 |
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 产品介绍 |
Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.
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| 产品图片 |
The purity of the protein is greater than 90% as determined by reducing SDS-PAGE.
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