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Rabbit
Anti-CPS1/FITC
Cat. Number:
bs-14034R-FITC
Quantity size:
100ul
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]
Also known as:
Carbamoyl phosphate synthase [ammonia];
Carbamoyl phosphate synthase [ammonia] mitochondrial;
Carbamoyl phosphate synthase;
Carbamoyl phosphate synthetase 1;
Carbamoyl phosphate synthetase 1 mitochondrial;
Carbamoyl phosphate synthetase I;
Carbamoyl-phosphate synthase [ammonia];
Carbamoyl-phosphate synthetase I;
Carbamoylphosphate synthase;
Carbamoylphosphate synthetase 1;
Carbamoylphosphate synthetase I;
CPS 1;
Cps1;
CPSase 1;
CPSase I;
CPSASE1;
CPSM_HUMAN;
mitochondrial;
MS738.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with:
(predicted: )
●
Immunogen: KLH conjugated synthetic peptide derived from human CPS1.
●
Predicted Molecular Weight: 160kDa.
Storage:
0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Application:
Excitation spectrum: 495nm
Emission spectrum: 519nm
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.